dyskeratosis congenita induced cirrhosis for liver transplantation-perioperative management
;Anshuman Singh;V K Pandey;Manish Tandon;C K Pandey
Veterinary radiology & ultrasound : the official journal of the American College of Veterinary Radiology and the International Veterinary Radiology Association2015Vol. 59pp. 312-314
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singh2015indiandyskeratosis
Abstract
Dyskeratosis congenita (DC) is an inherited disorder with progressive multisystem involvement. End stage liver disease (ESLD) in patients with DC is rare. We describe the perioperative management of a patient with DC induced ESLD and severe hepatopulmonary syndrome for living donor liver transplantation.