Moyamoya means hazy in Japanese. It is a rare progressive idiopathic condition that affects major intracranial vessels. The disease is characterized by the distinct angiographic appearance of cerebral vessels resembling "puff of cigarette smoke." Although rare, a high index of suspicion in correct clinical setting can be helpful in apt diagnosis. The disease cloaked in common symptoms can lead to a devastating outcome, both in children and adults. Hence, comprehensive knowledge of this peculiar entity is a must.