Introduction: Ectromelia is a congenital abnormality characterized by limb growth disturbances (aplasia or hypoplasia) during the period from 4th to 8th gestation week. Case outline. We present a case of hemimezomelic longitudinal ectromelia of the right upper limb associated with other skeletal abnormalities, surgically treated. An important role in the management of this case is attributed to the complex rehabilitation programme done before and after each surgical intervention. Conclusion. The aim of the complex therapy is to diminish the permanent invalidity of these patients. .