Myopericytoma is a rare tumour arising from myopericytes. Myopericytes are transitional cells between pericytes, which are perivascular cells adjacent to capillaries, and vascular smooth muscle cells. We report a case of cutaneous myopericytoma metastasising to the right kidney. It represents one of the few cases of malignant behaviour in myopericytoma, and is the first report of a myopericytoma metastasising to the urinary tract. This case suggests that the traditional view that urinary myopericytoma are benign lesions needs to be updated.